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> Immunohistochemistry (IHC) Antibody to Canine HSP60 Immunohistochemistry (IHC) Antibody to Canine HSP60
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Immunohistochemistry (IHC) Antibody to Canine (Dog) HSP60 Products
All HSP60 Products list
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Immunohistochemistry (IHC) Antibody to HSP60
– Immunohistochemistry (IHC) Antibody to Canine (Dog) HSP60
Browse Immunohistochemistry (IHC) Antibody to HSP60 Products by Following Categories
HSP60 Protein , Antibody, ELISA Kit, cDNA Clone
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Immunohistochemistry (IHC) Antibody to HSP60
– Immunohistochemistry (IHC) Antibody to Human HSP60
– Immunohistochemistry (IHC) Antibody to Mouse HSP60
– Immunohistochemistry (IHC) Antibody to Rat HSP60
– Immunohistochemistry (IHC) Antibody to Rhesus HSP60
– Immunohistochemistry (IHC) Antibody to Cynomolgus HSP60
– Immunohistochemistry (IHC) Antibody to Canine (Dog) HSP60
– Immunohistochemistry (IHC) Antibody to Ferret HSP60
– Immunohistochemistry (IHC) Antibody to Bovine HSP60
Antibody to HSP60
Immunohistochemistry (IHC) Antibody to HSP60 Related Products
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ELISA Antibody to HSP60
– ELISA Antibody to Human HSP60
– ELISA Antibody to Mouse HSP60
– ELISA Antibody to Rat HSP60
– ELISA Antibody to Rhesus HSP60
– ELISA Antibody to Cynomolgus HSP60
– ELISA Antibody to Canine (Dog) HSP60
– ELISA Antibody to Ferret HSP60
– ELISA Antibody to Bovine HSP60
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Western Blot Antibody to HSP60
– Western Blot Antibody to Human HSP60
– Western Blot Antibody to Mouse HSP60
– Western Blot Antibody to Rat HSP60
– Western Blot Antibody to Rhesus HSP60
– Western Blot Antibody to Cynomolgus HSP60
– Western Blot Antibody to Canine (Dog) HSP60
– Western Blot Antibody to Ferret HSP60
– Western Blot Antibody to Bovine HSP60
Flow Cytometry (FACS) Antibody to HSP60
– Flow Cytometry (FACS) Antibody to Human HSP60
– Flow Cytometry (FACS) Antibody to Mouse HSP60
– Flow Cytometry (FACS) Antibody to Rat HSP60
– Flow Cytometry (FACS) Antibody to Rhesus HSP60
– Flow Cytometry (FACS) Antibody to Cynomolgus HSP60
– Flow Cytometry (FACS) Antibody to Canine (Dog) HSP60
– Flow Cytometry (FACS) Antibody to Ferret HSP60
– Flow Cytometry (FACS) Antibody to Bovine HSP60
Browse HSP60 Antibody by Following Categories
HSP60 Antibody
– Human HSP60 Antibody
– Mouse HSP60 Antibody
– Rat HSP60 Antibody
– Rhesus HSP60 Antibody
– Cynomolgus HSP60 Antibody
– Canine (Dog) HSP60 Antibody
– Ferret HSP60 Antibody
– Bovine HSP60 Antibody
Additional HSP60 Products
Summary for HSP60
HSP60, also known as HSPD1, is a member of the chaperonin family. HSP60 may function as a signaling molecule in the innate immune system. This protein is essential for the folding and assembly of newly imported proteins in the mitochondria. It may also prevent misfolding and promote the refolding and proper assembly of unfolded polypeptides generated under stress conditions in the mitochondrial matrix. HSP60 gene is adjacent to a related family member and the region between the 2 genes functions as a bidirectional promoter. Several pseudogenes have been associated with this gene. Mutations associated with this gene cause autosomal recessive spastic paraplegia 13.Defects in HSP60 are a cause of spastic paraplegia autosomal dominant type 13 (SPG13). Spastic paraplegia is a degenerative spinal cord disorder characterized by a slow, gradual, progressive weakness and spasticity of the lower limbs. Defects in HSP60 are the cause of leukodystrophy hypomyelinating type 4 (HLD4); also called mitochondrial HSP60 chaperonopathy or MitCHAP-60 disease. HLD4 is a severe autosomal recessive hypomyelinating leukodystrophy. HSP60 is cinically characterized by infantile-onset rotary nystagmus, progressive spastic paraplegia, neurologic regression, motor impairment, profound mental retardation. Death usually occurrs within the first two decades of life.
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